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Hemifacial hypertrophy abbreviated as (HFH) is rare congenital disease characterized by unilateral enlargement of the head and teeth. It is classified as true. Depending on involvement of soft tissues, teeth, and bones, he further classified hemifacial hypertrophy into (a) true hemifacial hypertrophy and. Two cases of congenital hemifacial hypertrophy are described. To our knowledge , this is the first report of this syndrome in a black African population. Possible.

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These patients present with dental, skeletal, uemifacial soft tissues of the affected portion of the face [ 11 ]. Mouth opening and the range of movement was adequate.

Wider and thicker mandibular alveolar process on right side, particularly in the premolar-molar region. According to Rowe, the size and shape of the tooth crown and root size, as well as rate of development, are usually abnormal if the teeth are affected [ 3 ].

Burchfield D, Escobar V. Stern, Oral and Maxillofacial Pathology: The ideal conditions for the use of liposuction are the existence of sufficient elasticity of the skin; little excess skin and sufficient subcutaneous adipose tissue to be suctioned. Rowe[ 8 ] described abnormalities in the dentition of the abnormal side in three respects; the crown size, the root size and shape, and rate of development.

Please review our privacy policy. CT scan of the present case demonstrated prominent facial asymmetry which was caused by the unilateral enlargement of both soft tissue structures and the underlying skeleton of the right side of the face, along with dental involvement, making this case unique in its presentation.

Midline shift and altered occlusion with deviated occlusal plane are noticed. Santosh Ashok NandimathG. By using this site, you agree to the Terms of Use and Privacy Policy. Various etiological factors like heredity, chromosomal abnormalities, altered intrauterine development, endocrine dysfunction, and vascular and lymphatic abnormalities remain implicated in this lesion.


However, marked unilateral overdevelopment of the hard and soft tissues of the head and face is a rare congenital malformation variously described as facial hemihypertrophy, partial or unilateral gigantism, and hemifacial hyperplasia [ 5 ]. She gave a history of an abnormally enlarged left half of her face since birth which became more prominent following menarche.

The maxillary and mandibular midline was shifted to the left.

Congenital hemifacial hyperplasia

J Cutan Aesthet Surg. HFH may be associated with other conditions, such as acromegaly and pituitary gigantism, or with hypertrophy of other parts of the body [ 8 ].

The professed causes for this condition include inherited chromosomal abnormalities[ 1314 ] endocrine dysfunctions, vascular or lymphatic malformation, atypical forms of twinning, altered intrauterine environment, and disturbances of the central nervous system[ 1516 ] Pollock et al.

Hemifacial hyperplasia or hemifacial hypertrophy is a rare developmental anomaly characterised by asymmetric growth of hard and soft tissues of the face 1. The etiology of congenital hemifacial hypertrophy and hypdrtrophy case report. Hypertropy J Maxillofac Surg. The teeth, mandible, and maxilla should be carefully scrutinized for deformities to help one reach the correct diagnosis.

Case Reports in Dentistry

Infobox medical condition new. The teeth on the affected side had matured earlier, were larger, and had erupted prematurely with early loss of the deciduous teeth followed by replacement of permanent dentition as compared to the normal side.

Loading Stack – 0 images remaining. C ase R eport A year-old female patient presented to the Department of Oral and Maxillofacial Surgery with a chief complaint of asymmetry of her face. Received Jul 26; Accepted Sep Hemifacisl hemihyperplasia is a rare developmental disorder hypertropy by unilateral overgrowth of one or more body parts resulting in marked asymmetry. The purpose of this report is to present the case of a child with congenital hemifacial hyperplasia and to supplement existing clinical knowledge.

Periapical, mandibular and maxillary hard tissues — Bones of jaws. An embryologic hypothesis and case report.

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Tommasi AF, Jitomirski F. Review and report of two cases. This change in the physical properties of the cell membrane then appears to cause a complex enzymatic cascade involving the release of lipases and other enzymes as well as a hyppertrophy apoptotic cascade that causes adipocyte cell death.


View at Google Scholar O. Asymmetry is one of the more unusual and interesting errors of human reproduction. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Histologic examination in one case demonstrated that the enlargement resulted from an increased number of cells rather than an increase in cell size. However, the unilateral distribution of dental anomalies and the concurrent unilateral tongue enlargement are the prominent features which make HFH an unique entity [ 3 ].

Occlusal view of the maxillary and mandibular dental casts showing macrodontia of the right side, midline shift to the left, along with granular surface of the right palatal mucosa.

Routine blood investigations were also under normal limits. The tissue surrounding the teeth when compared with the left side was enlarged. Based on the clinical and radiographic features, the patient was provisionally diagnosed with true hemifacial hypertrophy of the left face. There was monstrous enlargement of the soft tissue over the zygoma, the infraorbital region and the symphyseal region.

Congenital isolated hemifacial hyperplasia. Support Center Support Center. Open in a separate window. Noticeable enlargement of tongue with the well-demarcated midline. Treatment modalities The treatment modalities extend from subtle soft tissue contouring to extensive surgeries to correct the underlying bony defect and reshape the overlying soft tissues. CT scan exhibits enlarged petrous part of temporal bone, pituitary fossa, maxilla, and mandible.